ABSTRACT
Bleeding disorders are commonly associated with hemato-oncologic diseases. We report a 68 years old male with a chronic myelomonocytic leukemia derived from a long lasting mielodysplastic syndrome that did not respond to treatment with Azacitidine. The patient was hospitalized due to tonic clonic seizures. A CAT scan showed a hematoma in the frontal lobe. A new assessment of hemostasis revealed an isolated deficiency of Factor X. We speculate that this deficit could be secondary to consumption due to the chronic Myelomonocytic Leukemia.
Subject(s)
Aged , Humans , Male , Factor X Deficiency/etiology , Frontal Lobe/injuries , Leukemia, Myelomonocytic, Chronic/complications , Antimetabolites, Antineoplastic/therapeutic use , Azacitidine/therapeutic use , Factor X Deficiency/diagnosis , Hematoma/diagnosis , Leukemia, Myelomonocytic, Chronic/drug therapy , Leukocytes , Monocytes , Seizures/complicationsSubject(s)
Humans , Female , Middle Aged , Leukemia, Myelomonocytic, Chronic/pathology , Xanthomatosis/pathology , Arthritis/complications , Erythema Nodosum/complications , Fatal Outcome , Leukemia, Myelomonocytic, Chronic/complications , Serositis/complications , Vasculitis/complications , Xanthomatosis/complicationsABSTRACT
El objetivo del presente reporte es la descripción de un paciente de la Clínica Pediátrica "B" del hospital "Pereira Rossell", portador de la asociación: Neurofibromatosis de Von Recklinghausen (NF); Xantogranulomatosis Cutánea Juvenil (XCJ) y Leucemia Mielomonocítica Crónica Juvenil (LMMCJ)